Benign Mesothelioma of Mahaim

[A multicystic tumor arising in the inferior interatrial septum in the region of the atrioventricular node. The vast majority of patients present with complete heart block and a minority with partial heart block. Sudden death is reported in approximately 10% of the cases. It is a morphologically benign tumor composed of cuboidal, transitional, or squamoid cells. The cells may also show sebaceous differentiation and originate from the endoderm. ( NCI )]

UMLS (NCI) C1266075

Cystic Tumor of Atrioventricular Node
Endodermal Rest
Intracardiac Endodermal Heterotopia
Mesothelioma of Atrioventricular Node
Tawarian Node