[A neoplasm with perivascular epithelioid cell differentiation, often associated with tuberous sclerosis. It is characterized by the presence of smooth muscle and epithelioid cells, and the proliferation of lymphatic vessels. Sites of involvement include the lymph nodes, lung, mediastinum, and retroperitoneum. ( NCI )]
UMLS (NCI) C0024223 Relation/PAR: Lymphoproliferative Disorder
Lymph Vessel Neoplasm
Relation/CHD: LAM